Papillary tumor of the pineal region: report of a rapidly progressive tumor with possible multicentric origin

• DOI: 10.1007/s00247-008-1060-1
• Publication Date: 2008-11-26T12:23:52Z
• Authors: Takashi S. Sato; Patricia A. Kirby; John M. Buatti; Toshio Moritani
• Keywords: Male; Brain Neoplasms; Pentetic Acid; Magnetic Resonance Imaging; Pineal Gland; Carcinoma, Papillary; 03 medical and health sciences; Fatal Outcome; 0302 clinical medicine; Humans; Radiopharmaceuticals; Radionuclide Imaging; Pinealoma

Papillary tumor of the pineal region (PTPR) is an uncommon tumor recently added to the WHO classification of CNS tumors. We report a case of PTPR in a young boy that was noteworthy for early CSF dissemination and relentless progression. In spite of intensive chemotherapy and comprehensive radiotherapy, the boy died. The neuroimaging appearance is unique with possible multicentric origin of the tumor and intense uptake of (111)In-DTPA-pentetreotide.