Malignant triton tumor of the kidney in a child: A case report

• DOI: 10.1016/j.ijscr.2021.106252
• Publication Date: 2021-07-30T06:25:13Z
• Authors: Rafael Bittencour...; Carlos Eduardo Pi...; Leonardo Dantas d...; Marina Bertuol; Paola Maria Broli...; Eliziane Emy Taka...
• Keywords: Abdominal mass; Concomitant

Malignant triton tumor (MTT) is an extremely rare variant of the malignant peripheral nerve sheath tumors (MPNSTs) with rhabdomyosarcomatous differentiation, which was first described in 1932 by Mason. MTT affects, most cases, patients under 35 years age, and it usually manifested as a mass that may or not be painful. However, incidence pediatric atypical. This presents aggressive course limited survival rate, prognosis different between individuals without concomitant diagnosis neurofibromatosis type 1 (NF1). Currently, recommended treatment surgical resection, adjuvant chemotherapy radiotherapy, but its efficacy yet clear.A 13-year-old female patient referred to oncology service due presence abdominal weight loss, initially diagnosed Wilms' tumor. After extensive investigation, immunohistopathological evaluation, confirmed. The also underwent cycles after currently awaiting immunotherapy.Malignant difficult diagnose, especially children young people, age groups disease even lower. reason rarely suspected, great challenge for clinical care team. It essential consider investigate this possibility differential diagnosis, have low rate poor prognosis.