Giant major aortopulmonary collateral artery: A rare cause of heart murmur in newborns

• DOI: 10.1016/j.repce.2014.02.009
• Publication Date: 2014-08-19T00:15:20Z
• Authors: Luís Martins; Rita S. Oliveira; Patrícia Silva; Joana Marinho; Graça Sousa; Eduardo Castela
• Keywords: Radiography; Heart Murmurs; Infant, Newborn; Humans; Abnormalities, Multiple; Aorta, Thoracic; Female; Pulmonary Artery; 3. Good health

s p c t a s t e P Major aortopulmonary collateral arteries (MAPCAs) are anomalous vessels that develop from the aorta or its main branches and supply the pulmonary parenchyma with oxygenated blood. They are usually associated with congenital heart disease and are rare in isolation. We report the case of a newborn girl, full term, with no relevant history, in whom a III/VI murmur was detected on the left sternal border on the first day of life. At seven days a remote cardiology consultation raised the suspicion of right inferior pulmonary vein stenosis despite normal pulmonary artery systolic pressure. Echocardiography in the Hospital Pediatrico Carmona da Mota showed ‘‘an anomalous vessel draining into the right inferior pulmonary vein’’. At one month of age computed tomography angiography revealed a single MAPCA emerging from the celiac trunk to