Systemic Juvenile Xanthogranulomatosis Imitating a Malignant Abdominal Wall Tumor With Lung Metastases

• DOI: 10.1097/mph.0b013e318030ac5e
• Publication Date: 2007-01-17T09:03:16Z
• Authors: Nicola J. Matcham; Savvas Andronikou; Keith Sibson; Pramila Ramani; David Grier
• Keywords: Sarcoma/radiography; Lung Neoplasms; Tomography Scanners, X-Ray Computed; Abdominal Wall; Sarcoma; 3. Good health; Radiography; 03 medical and health sciences; Abdominal Neoplasms/*radiography; 0302 clinical medicine; Xanthogranuloma, Juvenile/*radiography; Abdominal Neoplasms; Child, Preschool; *Abdominal Wall; Humans; False Positive Reactions; Female; Neoplasm Metastasis; *Tomography Scanners, X-Ray Computed; Xanthogranuloma, Juvenile; Lung Neoplasms/*radiography/secondary

Juvenile xanthogranulomatosis (JXG) is a rare benign condition, which usually presents with characteristic skin lesions and can be diagnosed clinically. However, systemic JXG may involve wide range of extracutaneous sites pose diagnostic dilemma for the clinician, radiologist, pathologist. In particular it simulate malignancy. Here, we report case within abdominal wall musculature lungs, imitated sarcoma pulmonary metastases on computerized tomography. To best our knowledge, this first such reported case. particular, disease presenting without unusual.