Sturge‐Weber‐Dimitri disease without facial nevus

• DOI: 10.1212/wnl.37.6.1063
• Publication Date: 2012-05-13T12:43:07Z
• Authors: A. B. Taly; D. Nagaraja; S. Das; S. K. Shankar; N. G. Pratibha
• Keywords: Male; Angiomatosis; Nevus, Pigmented; Brain; Calcinosis; 3. Good health; 03 medical and health sciences; 0302 clinical medicine; Sturge-Weber Syndrome; Child, Preschool; Humans; Facial Neoplasms; Tomography, X-Ray Computed

A patient with Sturge-Weber-Dimitri disease presented with intractable seizures and progressive intellectual deterioration. There was no facial nevus or focal neurologic abnormality. CT disclosed bilateral calcification in a parieto-occipital gyral pattern. Histopathology of the brain revealed extensive calcification of vessel wall in parieto-occipital cortices.