Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma

• DOI: 10.3389/fcvm.2021.709328
• Publication Date: 2021-10-25T05:48:55Z
• Authors: Jorge Cossío-Aranda; Alberto Aranda-Fr...; Joaquin Berarducci; Nilda Espinola-Za...; Laila González-Me...; Clara Vázquez-Antona; Gabriela Meléndez...; Javier Ivan Armen...; Candace Keirns
• Keywords: Rhabdomyoma; Rare disease

We present the case of a young male patient with an initial diagnosis rhabdomyoma that was surgically treated at different hospital when he 17. After 2-year disease-free period, presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies both tumors led to primary malignant cardiac PEComa histopathologic characteristics resembled abundant "spider cells."