Ruptured aortic aneurysm in an adolescent with systemic lupus erythematosus

• DOI: 10.5546/aap.2024-10379.eng
• Publication Date: 2024-10-14T15:54:17Z
• Authors: Laura Mónica Pérez; Marta L. Fiorotto; Giselle Villarreal; María Martha Kats...; Pedro Rino

Systemic lupus erythematosus (SLE) is a chronic, multisystem, autoimmune disease. Cardiovascular involvement frequent; however, aneurysm and/or aortic dissection are rare entities with fatal evolution. The objective to describe and complication of SLE in pediatrics review the literature. We present case 16-year-old girl multisystem without cardiovascular disease at diagnosis. She consulted for severe chest pain. Chest X-ray showed dilated arch no cardiomegaly. presence was suspected, an angiotomography performed. A descending flap confirmed. Antihypertensive treatment started. After Valsalva maneuver, she presented aneurysmal rupture. died 12 hours after admission. Aneurysm infrequent complications pediatric SLE. As they have high mortality, it essential consider them patient