Pancreatoblastoma in children: EXPeRT/PARTNER diagnostic and therapeutic recommendations

Surgical resection Paediatric surgery Consensus conference
DOI: 10.1002/pbc.29112 Publication Date: 2021-06-26T17:18:16Z
ABSTRACT
Abstract Pancreatoblastoma (PBL) is a rare malignant epithelial neoplasm that affects typically young children. Signs related to advanced upper‐abdominal tumor accompanied by elevated serum α‐fetoprotein levels in child suggest PBL, however histopathological confirmation mandatory. The mainstay of the treatment complete surgical resection. Unresectable and/or metastatic PBL may become amenable delayed surgery after neoadjuvant chemotherapy. This manuscript presents international consensus recommendations for diagnosis and children with established European Cooperative Study Group Pediatric Rare Tumors (EXPeRT) within EU‐funded PARTNER (Paediatric Network – Registry) project.
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