A chylothorax in a young woman: The difficulties of medical management

• DOI: 10.1002/rcr2.1303
• Publication Date: 2024-02-16T06:00:33Z
• Authors: Eleanor C. Barton; Simon Johnson; Neil Collin; Nidhi Bhatt; Nick A. Maskell
• Keywords: Lymphangioleiomyomatosis; Chylothorax; Rare disease

Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax well-recognized complication the condition, management strategies aren't well-defined, have low success rates and are often only available at tertiary or specialist centres. We describe case young woman referred to pleural clinic with chylous effusion found be secondary lymphangioleiomyomatosis. Initial medical was unsuccessful recurrent drainages caused significant complications. Remission ultimately achieved combination mTOR inhibitors interventional radiology techniques.