Occlusion of the Left Main Coronary Artery Os By a Tethered Aortic Valve Cusp

• DOI: 10.1016/j.athoracsur.2013.10.108
• Publication Date: 2014-02-26T00:01:42Z
• Authors: Jonathan H. Soslow; Daniel L. Saurers; Debra A. Dodd; Thomas P. Doyle; David P. Bichell; Ann Kavanaugh-McHugh
• Keywords: Left coronary artery; Ventricular Function

We report a 4-month-old girl who presented with poor ventricular function and was found to have occlusion of the left main coronary artery os by a tethered aortic cusp. The patient underwent surgical delamination of the aortic valve leaflet, revealing a normal left coronary os. After operative repair, her left ventricular function improved significantly. This diagnosis should be included in the differential in all children presenting with cardiac dysfunction.