Endovascular fenestration and stenting for renovisceral malperfusion in a pediatric patient with type II Loeys-Dietz syndrome

• DOI: 10.1016/j.jvscit.2024.101514
• Publication Date: 2024-05-18T04:35:00Z
• Authors: Roberto G. Aru; Courtenay M. Hols...; Connor W. Smith; James H. Black
• Keywords: Fenestration

A 16-year-old girl with Loeys-Dietz syndrome presented an acute, complicated type B aortic dissection (AD) mesenteric and right renal malperfusion owing to a dynamic obstruction. The anatomy of her AD genetic aortography were suboptimal for thoracic endovascular repair. Given the concern anticipated late degeneration need open repair, she underwent successful transfemoral septal fenestration stenting into superior artery additional artery. Her failure angina resolved, was discharged home. Endovascular provides elegant solution AD-associated branch vessels without compromising future repairs.