A rare indication of permanent pacemaker implantation in children: congenital long QT syndrome

• DOI: 10.1017/s1047951120003108
• Publication Date: 2020-09-30T04:45:02Z
• Authors: Mehmet Taşar; Nur Dikmen Yaman; Huseyin Dursin; Murat Şimşek; Senem Özgür
• Keywords: Channelopathy; Torsades de pointes; Short QT syndrome; Sudden Death

Abstract Congenital Long QT Syndrome (LQTS) is a dangerous arrhythmic disorder that can be diagnosed in children with bradycardia. It characterised by prolonged interval and torsades de pointes may cause sudden death. syndrome an ion channelopathy complex molecular physiological infrastructure. Unlike the acquired type, congenital LQTS has genetic inheritance it syncope, stress activity, cardiac dysfunction, death or sometimes incidentally. Permanent pacemaker implantation required for resistant bradycardia even to resolve symptoms avoid