Laparoscopic Resection of Periadrenal Paraganglioma in a Patient With Multiple Endocrine Neoplasia Type 2A

• DOI: 10.1097/sle.0b013e3182074c72
• Publication Date: 2011-02-08T06:16:06Z
• Authors: Takeo Nomura; Mika Takahashi; Tadasuke Ando; Fuminori Sato; Sumie Fujii; Hiromitsu Mimata
• Keywords: Adult; Male; Paraganglioma; 03 medical and health sciences; 0302 clinical medicine; Adrenal Gland Neoplasms; Humans; Laparoscopy; Multiple Endocrine Neoplasia Type 2a; Pheochromocytoma

We report here a case of recurrent pheochromocytoma successfully managed by laparoscopic surgery in a patient with multiple endocrine neoplasia type 2A. A 25-year-old man presented with the contralateral adrenal mass after earlier right adrenalectomy. For the preoperative diagnosis of left adrenal pheochromocytoma, adrenal sparing surgery was considered. From the intraoperative laparoscopic view, we found that the tumor originated in periadrenal sympathetic ganglia, and laparoscopic excision of paraganglioma was successfully performed that preserved the integrity of normal adrenal gland. Extra-adrenal pheochromocytoma is rather rare in MEN 2A and it is important to identify precise intraoperative localization of pheochromocytoma with laparoscopic surgery.