Angiosarcoma arising from congenital primary lymphedema

• DOI: 10.1111/pde.13664
• Publication Date: 2018-09-14T20:49:34Z
• Authors: Pauline Janssens; Valérie Dekeuleneer; An Van Damme; Pascal Brouillard; Nicole Revencu; Philippe Clapuyt; Ingrid Ferreira; Fanny Ballieux; Miikka Vikkula; Liliane Marot; Marie Baeck; Laurence M. Boon
• Keywords: lymphangiosarcoma; Hemangiosarcoma; Skin -- pathology; Stewart-Treves syndrome; Antineoplastic Agents; Hemangiosarcoma -- diagnosis -- therapy; Upper Extremity; 03 medical and health sciences; Fatal Outcome; 0302 clinical medicine; Humans; Lymphedema; Child; Preschool; Skin; Dermatologie; angiosarcoma; Upper Extremity -- pathology; congenital; Lymphedema -- complications -- congenital; Infant; Lymphangiosarcoma -- diagnosis -- therapy; Lymphangiosarcoma; lymphedema; sirolimus; Anatomopathologie; Child, Preschool; Antineoplastic Agents -- therapeutic use; Female

AbstractWe herein report the case of a 3‐year‐old girl with atypical congenital right upper limb lymphedema who developed an angiosarcoma. Only a few cases have been reported following congenital form of lymphedema and only 4 in such a young child. We also summarize all cases of angiosarcoma associated with congenital lymphedema reported in the literature.