Modern Approaches in Management of Children with Cystic fibrosis

• DOI: 10.15690/pf.v19i2.2417
• Publication Date: 2022-05-31T09:17:41Z
• Authors: Alexander A. Baranov; Leyla S. Namazova...; Sergey I. Kutsev; Sergey N. Avdeev; Elena V. Polevich...; Andrey S. Belevskiy; Elena I. Kondratyeva; Olga I. Simonova; Nataliya Yu. Kash...; Victoria D. Sherman; Anna Yu. Voronkova; Evgeniya L. Amelina; Tatyana E. Gembit...; Stanislav A. Kras...; Alexey G. Chermen...; Tatyana A. Stepan...; Liliia R. Selimzy...; Elena A. Vishneva; Yulia V. Gorinova; Elena A. Roslavtseva; Irina K. Asherova; Natalya A. Ilyenkova; Sergey K. Zyryanov; Niso D. Odinayeva; Tatyana Yu. Maksi...; Alexander V. Orlov; Sergey Yu. Semykin; Marina Yu. Chernukha; Igor A. Shaginyan; Lusine R. Avetisyan; Galina L. Shumkova; Natalya A. Krylova; Ivan A. Dronov; Maria N. Kostyleva; Ludmila A. Zhelenina; Nikolay N. Klimko; Yuliya V. Borzova; Natalya V. Vasilyeva; Tatyana S. Bogomo...; Anna A. Speranskaya; Irina A. Baranova; Evgeny G. Furman; Vera V. Shadrina; Nikolay F. Shchapov; Nika V. Petrova; Ivan V. Pashkov; Olga M. Tsirulnikova; Dmitriy P. Polyakov; Valeriy M. Svistu...; Eduard V. Sin'kov; Vyacheslav B. Che...; Svetlana A. Repina; Dmitriy A. Blagov...; Mikhail P. Kostinov; Olga V. Kondratenko; Artem V. Lyamin; Svetlana V. Polik...; Alexander V. Poly...; Tagui A. Adyan; Dmitry V. Goldshtein; Tatiana B. Bukharova; Anna S. Efremova; Elena S. Ovsyankina; Ludmila V. Panova; Irina V. Cherkashina
• Keywords: Etiology; Pathogenesis

The problem of timely diagnosis and proper management patients with cystic fibrosis is crucial not only in our country, but throughout the world. Experts Union Pediatricians Russia have considered various issues etiology, pathogenesis, epidemiology, diagnosis, treatment this genetic disease a modern light. Particular attention was paid to screening methods for early fibrosis. principles complex therapy were justified, including rational use antibacterial mucolytic drugs enzyme replacement that significantly determine prognosis.