Surgical Treatment for Hemophilic Pseudotumor

• DOI: 10.2106/jbjs.16.01299
• Publication Date: 2017-06-07T15:32:29Z
• Authors: Jiliang Zhai; Xisheng Weng; Baozhong Zhang; Yong Liu; Peng Gao; Yan-yan Bian
• Keywords: Curettage; Bone grafting

Background: Hemophilic pseudotumor (HPT) is a rare disease with many challenges. Only few reports on surgical treatment for HPT have been published. Methods: The cases of 23 patients who had from July 1996 to December 2014 were retrospectively reviewed. Demographic data, blood loss and transfusion during surgery, outcomes, complications after surgery analyzed. Results: Eleven underwent resection; 4 excision, allograft transplantation, absorbable screw fixation; 3 resection metallic internal 2 resection, autogenous fibular grafting, curettage bone-grafting; 1 patient received above-the-knee amputation. average age (and standard deviation) the at time was 31.9 ± 12.8 years (range, 6 54 years) an follow-up 5.3 4.7 1.1 19.6 years). median duration 157 minutes 90 315 minutes). amount 800 mL 100 4,000 mL). Three (13%) postoperative infection, (8.7%) recurrence HPT, another fracture nonunion. Conclusions: Surgical modified protocol coagulation factor replacement safe effective. It should be recommended progressive enlargement mass, recurrent massive bleeding, spontaneous perforation, bone erosion, or compression surrounding tissues failure conservative treatment. Level Evidence: Therapeutic IV . See Instructions Authors complete description levels evidence.