Use of the Sheffield Telescopic Intramedullary Rod System for the Management of Osteogenesis Imperfecta

• DOI: 10.2106/jbjs.j.01893
• Publication Date: 2011-11-02T21:43:32Z
• Authors: Nicolas Nicolaou; John David Bowe; J Mark Wilkinson; James Alfred Fern...; Michael J Bell
• Keywords: Fracture Healing; Male; Reoperation; Equipment Safety; Infant; Equipment Design; Bone Nails; Osteogenesis Imperfecta; Internal Fixators; Fracture Fixation, Intramedullary; 3. Good health; Cohort Studies; Radiography; 03 medical and health sciences; Fractures, Spontaneous; 0302 clinical medicine; Child, Preschool; Humans; Equipment Failure; Female; Child; Follow-Up Studies; Retrospective Studies

Elongating intramedullary rods have been used in the management of osteogenesis imperfecta for past fifty years. The complication rates reported many reviews available techniques high. This study long-term functional outcomes and complications following use Sheffield system telescopic rods.We conducted a retrospective analysis patients with who were at least eighteen years age had thirteen follow-up. Complications, reoperations, data from disease-specific questionnaire Short Form-36 recorded.Data twenty-two treated an average nineteen after initial surgery. Reoperations involving thirty-three (50%) sixty-six performed: ten (15%) exchanged because rod disengagement due to growth, (20%) complications, required further surgery other than exchange complications. Mobility was significantly improved postoperative visit (p = 0.0015), this improvement maintained into adulthood 0.0077). Back pain most frequent symptom. Symptoms related insertion across knee ankle rare, but symptoms proximal femoral trochanteric entry common. Physeal damage not seen surgery, all elongated growth. All satisfied outcome surgical procedures. scores physical domains social function vitality worse those normal population.The technique are satisfactory adulthood; reoperation high commonly patient outgrowing rods. Concerns regarding fixed device unfounded, although fixation remains problem.