This paper proposed a probabilistic load flow analysis of correlated wind farms based on Copula theory. method addresses the linear and non-linear dependence between random variables more efficiently accurately than other methods. The is nearly unconstrained to marginal probability distribution types input variables. dependency established using theory in this paper. An improved Latin hypercube sampling adopted due real discrete data. Uncertainty factors are considered access power system...

In this paper, a probabilistic load flow analysis is proposed in order to deal with problems related the power system. Due increasing trend of penetration renewable energy sources system brought two factors: One uncertainty, and another one dependence. Uncertainty dependence factor increase risk associated operation planning. model these factors considered. Gaussian Copula theory establish probability distribution correlated input random variables. Three sampling methods are used Monte Carlo...

The present study aimed to examine and analyze cardiac involvement in two Emery‑Dreifuss muscular dystrophy (EDMD) pedigrees caused by the c.1583 C→G mutation of lamin A/C gene (LMNA). clinical genetic characteristics members families with EDMD were evaluated performing neurological examinations, skeletal muscle biopsies, evaluations, including electrocardiography, 24 h Holter, ultrasound cardiography 99TcM‑MIBI‑gated myocardiac perfusion imaging, genomic DNA sequencing. Family history...

The identification of disease-specific genetic and electrophysiological patterns for myotonia congenital (MC) could help clinicians apply in the findings studies to improve diagnosis. We examined molecular, clinical, histopathological characteristics eight patients with MC.Optimization PCR was used exclude myotonic dystrophies CLCN1 gene sequenced having clinical features indicative MC.Genetic screening identified nine mutations among patients, including two missense, three nonsense,...

Abstract Background Hereditary spastic paraplegia (HSP) is a group of neurodegenerative diseases characterized by lower-limb with highly genetic and clinical heterogeneity. However, the sign can also be seen in variety hereditary neurologic bilateral corticospinal tract impairment. The purpose this study to identify disease spectrum paraplegia, broaden coverage testing recognize clinical, laboratorial, electrophysiological radiological characteristics increase positive rate diagnosis....

To explore the clinical and genetic characteristics of five families with primary periodic paralysis (PPP). We reviewed manifestations, laboratory results, electrocardiogram, electromyography, muscle biopsy, analysis from PPP. Five PPP included: hypokalemic type 1 (HypoPP1, CACNA1S, 1/5), 2 (HypoPP2, SCN4A, 2/5), normokalemic (NormoPP, Andersen-Tawil syndrome (ATS, KCNJ2, 1/5). The basic manifestations were consistent PPP, presenting paroxysmal weakness, or without abnormal serum potassium....

Floppy infant syndrome (FIS) comprises of a group disorders with common symptom generalized hypotonia at birth or in early life, which causes diagnostic challenge. In the current work, we aimed to describe clinical and histopathological characteristics FIS help improve diagnosis this condition.We collected information on characteristics, laboratory data, electrophysiological test results detailed skeletal muscle biopsy features 25 infants FIS. We then discussed final diagnoses analyzed...

Non-intrusive load monitoring is an important development direction of electric monitoring. Traditional NILM mainly track and decompose the power voltage current, other transient or steady-state parameters like at system entrance, then identify specific type load. The identification method complicated, there are limitations on identifying multiple devices switching simultaneously. This paper studied oriented residential methods proposed one based periodogram, made detailed theoretical...

Although Vehicle Named Data Network (VNDN) possess the communication benefits of and Opportunity Network, it also introduces some new privacy problems, including identity security Requesters Providers. providers in VNDN need to sign data packets directly, which will leak information providers, while vicinity malicious nodes can access sensitive by analyzing relationship between names Interest Packages that are sent directly plaintext. In order solve above this paper presents an protection...

Ryanodine receptor 1 (RYR1), myosin heavy chain 7 (MYH7), and selenoprotein N1 (SEPN1) mutations are associated with core myopathies. RYR1 cause most cases of central disease (CCD).We screened 8 Chinese patients clinicopathological diagnosis CCD. Genetic analysis was carried out by targeted next generation sequencing (NGS) to identify causative genes. Variants were assessed for pathogenicity using bioinformatic approaches, NGS results confirmed Sanger sequencing.One novel (p.L4578V)...

This paper presented a novel image enhancement algorithm using information fusion (fusionEnhance) to preserve edges in the filtering. The proposed firstly defined fuzzy-based region entropy inspired by concept of local and direction gradient respectively as sources, then it implemented triangle module operation for edge detection. Besides fusion-decision detection, operated modified hybrid filter method Experiment results illustrate that fusionEnhance can improve performance terms PSNR two...

Smart Grid is the latest direction for future power system development. The expansion of wireless broadband access and trunk in will improve not only working efficiency within enterprise network but also economic enterprises. In this paper, firstly major problems communication were presented. Then, architecture, key technologies as well technical advantages McWiLL multimedia proposed. Finally, combined with business requirements Grid, application prospects technology was

In order to effectively distinguish the objects from background, three transition region feature models were taken into account in this paper, including gradient, local complex and fuzzy variance. Firstly, used smooth region. Secondly, experimental results signified that every had effects on extracting background each model some disadvantages droplets (or watermarks) hydrophobic images. Finally, these combined together form domain for C-means clustering (FCM), then FCM was applied...

Global Energy Internet (GEI) is the trend of development energy industry with broad prospects and potential economic benefits social in world. It crucial to establish technical standard system GEI for technology innovation industrial development. First, systems standards at home abroad have been combed field ultra-high voltage transmission, smart grid clean energy. Secondly, brief analyses on benefit analyzed establishment system. Through discussion, content methodology are clarified clear...

The dispersion and real-time variation of the resident load bring some difficulties to management. Orienting energy internet, Equipment for residential can achieve centralized management unified dispatch as well using aggregated characteristics make more effective service in intelligent electric business demand side operations. According equipment with Energy Internet, this paper proposes five kinds aggregation modes combined hierarchy analysis thought user electricity infrastructure. What's...

A new two-dimensional chaotic system is proposed and used in the secure communication this paper. Because of high Lyapunov exponent, complex signal nonlinear spread spectrum technology, it enhances randomness unpredictability chaos carrier signals. Based on it, a masking encrypted method developed. The simulation results show that encryption effect well, recovered information less different from original signal. This has safety performance wide application.

In this study, a new concept of statistical distribution payback period is calculated for AC–DC transmission and asset expansion projects. For calculation the period, uncertainty considered with cost benefit. The Gaussian correlated input benefit variates. more examination point view, different correlation coefficients between main advantage study to draw probability function in terms because most industrialist are often interested analysis An example evaluation proposed model.

To investigate the clinical, pathological and genetic characteristics in a family with autosomal dominant Emery-Dreifuss muscular dystrophy (AD-EDMD).Clinical data skeletal muscle specimens were collected from two patients (the proband her daughter) for analysis. DNA samples of members (7 persons 3 generations) obtained PCR amplification direct sequencing lamin A/C (LMNA) gene. Haplotype analysis was performed after identification mutation.The had typical clinical manifestation EDMD: joint...

Objective To investigate the clinical manifestations and laboratory examinations of Duchenne muscular dystrophy (DMD) patients evaluate principle intermittent intravenous combined with oral glucocorticoid therapy. Methods The features, andfollow-up data 155 DMD were collected. These given dexamethasone 5-10 mg/d by infusion for 10-15 d prednisone acetate 0.50-0.75 mg/(kg·d) one month. After treatment, motor ability lower limbs, level serum creatine kinase (CK) 99mTc-MIBI gated myocardial...