[The audiological characteristics of large vestibular aqueduct syndrome in infants and young children].

• DOI: 10.13201/j.issn.1001-1781.2016.21.009
• Publication Date: 2016-11-05
• Authors: J X Liu; Lihui Huang; Xinxing Fu; H Liu; Yanfeng Yang; Xiaohua Cheng; Tianming Ni
• Keywords: Vestibular aqueduct; Auditory brainstem response; Unilateral hearing loss; Hearing level

Objective:To investigate the audiological characteristics of large vestibular aqueduct syndrome(LVAS) in infants and young children, to provide suggestion for early diagnosis intervention.Method:One hundred twenty-four cases diagnosed as LVAS were enrolled our study. Acoustic immittance, pediatric audiometry and(or) auditory steady state responses brainstem response test tested analyze degree configuration hearing loss, air-bone threshold difference short latency negative response.Result:The includes 44.8%(111/248) high frequency 19.0%(47/248) flat, 13.7%(34/248) rising, 3.6%(9/248) U type, which cannot be distinguished. The distribution loss total 124 (248 ears) 73.4%(182/248) profound 16.9%(42/248) severe 6.9%(17/248) moderate 2.8%(7/248)of mild loss. acoustically evoked ABR accounted 27.4%(68/248). emergence 24.6%(61/248), mean was(19.3±14.2) dB nHL.Conclusion:Infants children with syndrome mostly has curve, bone-air difference, that will remind clinicians LVAS.