- Congenital Heart Disease Studies
- Cardiac Arrhythmias and Treatments
- Cardiac pacing and defibrillation studies
- Renal and Vascular Pathologies
- Asthma and respiratory diseases
- Allergic Rhinitis and Sensitization
- Cardiovascular Issues in Pregnancy
- Dermatology and Skin Diseases
- Autoimmune Bullous Skin Diseases
- Infective Endocarditis Diagnosis and Management
- Mechanical Circulatory Support Devices
- T-cell and B-cell Immunology
- Coronary Artery Anomalies
- Pulmonary Hypertension Research and Treatments
- Cardiac electrophysiology and arrhythmias
- Cardiac Structural Anomalies and Repair
- Vascular anomalies and interventions
- Ion channel regulation and function
- Immunodeficiency and Autoimmune Disorders
- Cardiac Valve Diseases and Treatments
- Congenital Anomalies and Fetal Surgery
Bambino Gesù Children's Hospital
2018-2024
University of Rome Tor Vergata
2010
Abstract Aims The extracardiac conduit-Fontan (ECC) has become the preferred technique for univentricular heart palliation, but there are currently no data on incidence of long-term arrhythmias. This study investigated arrhythmias and relation to single ventricle morphology in follow-up (FU) ECC. Methods results All patients with ECC performed our Centre between 1987 2017 were included (minimum FU 5 years). Of 353 consecutive patients, 303 [57.8% males, aging 8–50 (median 20) years at last...
Abstract Aims The aims of this study are to evaluate the progressive involvement cardiac conduction system in Kearn–Sayre syndrome (KSS) and establish criteria for prevention episodes syncope or sudden death. Methods results This is a prospective monocentric including KSS patients, with diagnosis based on clinical manifestations, muscle biopsy, genetic tests, before age 18. All patients underwent screening examination 12-lead electrocardiogram (ECG), 24-h Holter monitoring, pacemaker (PM)...
Congenital heart disease (CHD) is the most common congenital anomaly at birth, affecting approximately 1% of live births. In recent decades great medical and surgical advances have significantly increased life expectancy, shifting healthcare professionals' researchers' interests in patients' Quality Life (QoL). The main aims our study were to evaluate generic condition-specific QoL a group Italian children adolescents with CHD their parents examine level agreement directional disagreement...
This study was designed to evaluate the difference in prevalence of long-term arterial hypertension among patients with corrected aortic coarctation according existence associated cardiac congenital lesions.We identified 235 who had undergone surgery for and classified them into 2 groups: isolated aorta (CoA) complex heart disease. Data were retrospectively analysed.There 148 subjects CoA 87 (CoA-c). Patients defined as hypertensive if they required antihypertensive treatment and/or when...
Background: In recent decades, aortic stenting has become a promising alternative to surgery for both native coarctation and re-stenosis in children adults. However, comparative long-term outcomes have poorly been investigated. Methods: We included 212 patients with previous repair (19 ± 8.7 years) divided into 3 groups: 139 single-time surgical (CoA-S group); 18 percutaneous (CoA-PS 55 hybrid multiple procedures because of re-coarctation occurrence (CoA-H group). All underwent 24-hour...
Abstract Funding Acknowledgements Type of funding sources: None. Background Arrhythmic complications, especially tachycardias, represent a common and important comorbidity during long-term follow up (FU) in patients with Fontan palliation for complexes congenital heart diseases (CHDs) univentricular hearts. Surgical technique has evolved from direct atrio-pulmonary connection via the intracardiac lateral tunnel to latest extracardiac conduit (ECC) procedure. Despite its shorter FU compared...
Objective: This study investigated hypertensive children for non-stenotic renal vascular abnormalities, in terms of number arteries, size, shape, course and possible relationships with arterial hypertension Design method: Patients referred elevated blood pressure were considered those known causes secondary excluded from the study. Seventy-two patients selected persistent (blood > 95th centile) more than one year's duration confirmed by 24 h ambulatory monitoring. All underwent abdominal...
Abstract Background Pacemakers (PMKs) and implantable cardioverter-defibrillators (ICDs) are frequently utilized in patients with specific cardiac rhythm disorders. The downfalls of these devices several but no data exist regarding leads thrombosis. Aim the study analysis pacing lead thrombosis occurrence paediatric PMK-ICD patients. Methods single Centre retrospective a series paediatric/young adult showing Data reported as median (interquartile range). Results from 2015 to 2021 five (2...