A5050159338- Congenital Heart Disease Studies
- Cardiac Valve Diseases and Treatments
- Congenital Diaphragmatic Hernia Studies
- Respiratory viral infections research
- Infective Endocarditis Diagnosis and Management
- Outsourcing and Supply Chain Management
- Viral Infections and Immunology Research
- Business Strategy and Innovation
- Mechanical Circulatory Support Devices
- Innovation and Knowledge Management
- Vascular anomalies and interventions
- Bacterial Infections and Vaccines
- Coronary Artery Anomalies
- Streptococcal Infections and Treatments
- Folate and B Vitamins Research
- Spinal Dysraphism and Malformations
- Spinal Hematomas and Complications
- Global Health and Epidemiology
- Blood disorders and treatments
- Global trade, sustainability, and social impact
- Management, Economics, and Public Policy
- Italy: Economic History and Contemporary Issues
- Platelet Disorders and Treatments
- Cervical and Thoracic Myelopathy
- Intestinal Malrotation and Obstruction Disorders
Miyazaki Prefectural Hospital
1997-2021
Hitotsubashi University
2018
University of Pennsylvania
1994
Miyazaki Welfare Medical College
1985-1994
University of Miyazaki
1985
Kabuki make-up syndrome has been reported mainly among Japanese, so far occurring in more than 20 cases. Among these, however, only one case associated with congenital heart defect reported. We have treated three patients this and of these two had disease. suggest the possibility that association disease may not be fortuitous.
To clarify the electroclinical manifestation of epileptic seizures and evolution epilepsy in patients with peroxisomal diseases.Retrospective review medical records EEGs 14 diseases: seven Zellweger syndrome (ZS), two neonatal adrenoleukodystrophy (NALD), acyl-CoA oxidase deficiency (AOXD), bifunctional enzyme (BFED), one rhizomelic chondrodysplasia punctata (RCDP). The diagnoses were made by biochemical analysis pathological examinations our laboratory.Patients manifested serious neurologic...
Disseminated intravascular coagulation (DIC) is a clinical condition with high mortality that characterized by the systemic activation of pathways resulting in multiple organ failure. Although no standard treatment for DIC has been established, recent reports have indicated recombinant human soluble thrombomodulin (rTM) effective against DIC.To elucidate characteristics and outcomes DIC, we retrospectively analyzed 92 patients who were treated rTM at Miyazaki Prefectural Hospital over 4-year...
Adhesive strapping for umbilical hernia has been re-evaluated as a promising treatment. We evaluated the influence of adhesive on outcome hernia.We retrospectively patients with referred to present institution from April 2011 December 2015. Patients who were treated compared an observation alone group. The group was also subdivided into two groups: cure and treatment failure group.A total 212 institution. Eighty-nine strapping, while 27 had only. rate in significantly higher than that...
An infant presented with a rare cervical (non-terminal) myelocystocele as congenital skin-covered mass located in the midline of posterior aspect her neck. Magnetic resonance (MR) imaging and computed tomography showed cystic filled cerebrospinal fluid neck, fibrous streak extending from bottom sac to dorsal surface cord. Brain MR also dilated ventricular system Chiari type II malformation. The patient underwent plastic repair lesion, which was diagnosed myelocystocele. After surgery,...
A 13-year-old girl developed viral myocarditis complicated by pulmonary thromboembolism. Marked dilatation and reduction in the contractility of left ventricle were noted a two-dimensional echocardiogram on admission. The thicknesses interventricular septum both 8 mm at this time, but increased after 9th day illness to reach 2 cm 15th day, with concomitant ventricular cavity. myocardial thickening gradually decreased ejection fraction improved serial echocardiographic evaluations, wall...
Abstract A sister and brother with neonatal alloimmune thrombocytopenic purpura (NAITP) caused by maternal anti‐human platelet antigen (HPA)‐3a are reported. The children had transient severe thrombocytopenia in the newborn period, were treated intravenous γ‐globulin concentrates from random donors. Although intracranial hemorrhage on day 2 postnatally, development of child has been normal no neurological sequelae have observed. only bloody stool when count was low, did not hemorrhagic...
Spontaneous spinal epidural hematoma (SSEH) is considered to be a relatively rare disease that can result in serious neurological sequelae. The pathogenesis and risk factors of SSEH are still unknown, its differential diagnosis varies widely. Misdiagnosis with more common conditions such as stroke or aortic syndromes occur. We report the case 27-year-old man who developed sudden upper back pain no specific precipitant. Five days later, he visited our emergency department complaining weakness...
The function of 9 St. Jude prosthetic mitral valves in 8 children was evaluated by continuous wave Doppler (CWD) echocardiography 28 +/- 22 months after implantation. All were apparently functioning normally on clinical examination. Peak flow velocity, mean pressure half-time and gradient determined from the transmitral velocity curve CWD echocardiography. For comparison, same parameters examined 15 normal 14 adults who had undergone valve replacement. measured values greater replacement...
先天性心疾患(congential heart disease:CHD)に合併した蛋白漏出性腸症(protein-losing enteropathy:PLE)は予後不良な疾患で, 病態についても不明な点が多く, 治療法もいまだ確立されたものはない. 著者らは, 完全型房室中隔欠損症, 両大血管右室起始症, 肺動脈閉鎖症に対するRastelli術後PLEの再燃時にヘパリン療法を施行し, 奏効した症例を経験した. しかし, 一旦中止後3カ月目に再々燃し, ステロイド療法,(ヘパリン＋ステロイド少量)併用療法, ヘパリン療法を施行したが, 効果は得られず死の転帰をとった. ヘパリン療法の問題点は, 完全寛解率は低く, 症状改善を維持するためには頻回投与が必要で, 皮下注投与量も多く, 患者負担が大きいことであった. CHD術後PLEに対するヘパリン療法には限界があった.