- Neonatal Respiratory Health Research
- Congenital Diaphragmatic Hernia Studies
- Child and Adolescent Health
- Adolescent and Pediatric Healthcare
- Maternal and Neonatal Healthcare
- Childhood Cancer Survivors' Quality of Life
- Neonatal and Maternal Infections
- Neuroscience of respiration and sleep
- Child Nutrition and Water Access
- Healthcare during COVID-19 Pandemic
- Genetic Syndromes and Imprinting
- NF-κB Signaling Pathways
- Bone fractures and treatments
- Health Education and Validation
- Bone Tumor Diagnosis and Treatments
- Global Maternal and Child Health
- Chronic Disease Management Strategies
- Women's cancer prevention and management
- Sleep and related disorders
- Acute Lymphoblastic Leukemia research
- Histiocytic Disorders and Treatments
- Bone Metabolism and Diseases
- Sepsis Diagnosis and Treatment
- Infant Development and Preterm Care
- Orthopedic Surgery and Rehabilitation
Centro Hospitalar Lisboa Norte
2013-2021
Hospital de Santa Maria
2008-2020
Hospital de São João
2003
Introdução: A Atenção Primária à Saúde (APS) é um modelo essencial no sistema de saúde, com foco na promoção da saúde e prevenção doenças, incluindo o combate às Doenças Sexualmente Transmissíveis (DSTs). No contexto sexual reprodutiva, a APS uma estratégia crucial para melhorar acesso conscientização população sobre DSTs, promovendo comportamentos sexuais seguros detecção precoce infecções, como HIV. Diante disso, presente estudo visa explorar Básica pode transformar reduzindo incidência...
McCune-Albright syndrome is a rare sporadic disease characterized by fibrous bone dysplasia, café-au-lait skin spots and variable hyperfunctional endocrinopathies. caused somatic postzygotic activating mutations in the GNAS gene that produce broad spectrum of effects.We report case with multi-organ manifestations neonatal period. A newborn preterm black girl was referred to our Neonatal Intensive Care Unit at age 17 days for suspected extrahepatic cholestasis. On clinical examination she...
Introdução: Fruto da mudança epidemiológica, o interesse pelas doenças crónicas complexas no sistema de saúde pediátrico tem vindo a crescer. Assim, pretendemos avaliar utilização do internamento hospitalar Serviço Nacional Saúde (Portugal Continental) por doentes pediátricos (0 – 17 anos) com complexas.Material e Métodos: Estudo epidemiológico observacional longitudinal retrospetivo (base dados morbilidade anonimizada). Selecionámos episódios pediátricos, entre 2011 2015; excluímos...
Cardoso, Bruno Miguel; Dupont, Juliette; Castanhinha, Susana; Ejarque-Albuquerque, Margarida; Pereira, Sónia; Miltenberger-Miltenyi, Gabriel; Oliveira, Graça Author Information
Subcapsular haematoma of the liver rarely occurs in neonates and diagnosis is often missed or delayed. It a catastrophic condition that can be caused by maternal, placentar fetal factors. A high index suspicion essential for early identification stabilisation babies with such pathology. In newborn hypovolemic shock abdominal distension, haemoperitoneum should suspected and, along exclusion other aetiologies, supportive therapy instituted. The hepatic subcapsular has non-specific...
A neonate with a prenatal diagnosis of left renal agenesis was born at 33 weeks gestation. postnatal abdominal ultrasound confirmed the absence kidney and revealed two non-divergent hemiuteri, consistent Herlyn-Werner-Wunderlich syndrome. During admission, significant axial hypotonia noted, warranting additional investigations. Brain ultrasounds MRI were normal, as preliminary metabolic study comparative genomic hybridisation array. DNA methylation testing Prader-Willi The baby discharged...
Introduction: Birth weight is a major contributor to neonatal morbidity and mortality associated with chronic diseases in adulthood. This study aimed evaluate the use of Intergrowth 21st instead Fenton & Kim 2013 growth charts diagnosis small large for gestational age group Portuguese newborns.Material Methods: We conducted an analytical retrospective birth term preterm newborns using both charts. Groups studied: ‘Term-weeks’ ‘Term-days’ (term weeks days, respectively), ‘Preterm-weeks’...
Objectives : To evaluate the respiratory support strategy and its association with morbidity mortality in preterm infants Gestational Age (GA) ≤ 32 weeks, admitted between 2000 2008. Methods Chart data from newborns GA weeks to a tertiary Neonatal Intensive Care Unit 2000-2008, were reviewed retrospectively. Newborns divided into two groups according year of birth: Group 1 (2000-2004) 2 (2005-2008). Each group was subdivided subgroups their GA: 23-28 gestational 29-32 weeks. compared terms...
A ocorrencia de neoplasias em mulheres gravidas e uma situacao rara, existindo tendencia para se tornar mais frequente, com a existencia um numero crescente gravidezes idades tardias. utilizacao farmacos citotoxicos durante gravidez representa riscos obvios o feto desenvolvimento, sobretudo fase organogenese. Apresenta-se caso clinico crianca nascida nao vigiada medicamente, tendo mae feito terapeutica citotoxica segundo terceiro trimestres da por recidiva leucemia mielomonocitica aguda. Nao...
Objectivos: Determinar o desenvolvimento neuro-motor e sensorial aos 36 meses de idade recem-nascidos (RN) pre-termo, com gestacional < 32 semanas, Hemorragia Intraventricular (HIV) grau III hidrocefalia pos-hemorragica (HPH). Material metodos: Foi efectuada a analise retrospectiva dos processos clinicos todos os RN pre-termo internados na Unidade Cuidados Especiais Recem-Nascidos (UCERN) do Hospital Santa Maria (HSM) 1 Janeiro 1990 31 Dezembro 1997. Dos 39 HIV, 11 (28,2%) faleceram e, em 19...
<h3>Background and Aims</h3> Early onset sepsis is a serious condition, with challenging diagnosis. C-Reactive Protein cut-off values for treatment vary according to different authors protocols from 5 mg/L 50 mg/L. The objective of this study was determine the CRP value in septic screening term near NB. <h3>Methods</h3> All NB gestational age (GA) ³ 35 weeks admitted nursery tertiary hospital course one year, risk early neonatal where included. We collected data all analysis (CRP/CBC) until...
Abstract Background The expected rise in the number of children living longer with complex chronic conditions (CCC) and social relevance this group prompt study patterns their inpatient care utilization. We aimed to compare utilization by CCC between regions mainland Portugal. Methods Observational longitudinal retrospective using anonymized administrative data for Portuguese public hospitals. selected admissions within pediatric age limit (&lt;18yo), 2011-15. variable interest was...
Abstract Diaphragmatic eventration is an anomaly of the diaphragm. In Scimitar syndrome, a curved-shaped anomalous pulmonary venous drainage seen. Association between these conditions rare. We present newborn with diaphragmatic eventration, whose diagnosis syndrome was made after surgical repair. congenital disorder often associated other heart and lungs anomalies. Diagnosis can be fortuitous but important prognostic features.
Os autores fazem a analise da casuistica neonatal do Hospital de Santa Maria nos ultimos 5 anos.O numero medio nados-vivos foi 2774. A taxa mortalidade perinatal tardia variou entre 7,4 e 12,8%0. entre3,1 5,3%o. percentagem recem-nascidos internados na Unidade Cuidados Especiais ao Recem-Nascido (UCERN) tem vindo diminuir, dadaa restricao dos criterios admissao, apesar internamento criancas idade gestacional cada vez mais baixa. geral UCERN varioude 3,7% 7,4%.A sobrevivencia media grupo...