Purpose: Home-based prophylaxis in hemophilia facilitates the treatment of patients with (PwH) at home resulting an improved quality life, experiencing less pain and greater flexibility daily activities. This literature studies cost effectivity adherence to after implementation home-based therapy PwH registered under Hemophilia Treatment Centre (HTC) Assam Medical College Hospital. Materials Methods: their parents were advised for self/home infusion being trained by a medical professional 6...

Objectives: To study the bone mineral density in patients with thalassemia. Thalassemia is a genetic disorder characterized by reduced synthesis of globin chain, leading to decreased hemoglobin levels. Blood transfusion therapy primary treatment, but it can cause iron overload and other factors that increase risk low density. Despite this, there limited research on thalassemia India, particularly North Eastern region, focus Material Methods: We conducted hospital-based case-control...

Background: The COVID-19 pandemic and its accompanying lockdown measures adversely affected institution-based education system including medical education. Internet-based online teaching emerged as the only alternative mode of continuing during those times. situation was novel to institutions, faculties, well students involved coordinated effort from all stakeholders for an efficient outcome ritual compulsory Aims Objectives: study planned obtain perspective point view various aspects MBBS...

The Journal is the primary organ of Continuing Paediatric Medical Education in Sri Lanka. journal also has a website. Free full text access available for all readers.The Lanka Child Health now indexed SciVerse Scopus (Source Record ID 19900193609), Index Medicus South-East Asia Region (IMSEAR), CABI (Centre Agriculture and Bioscience International Global Database), DOAJ Google, as well Google Scholar.The policies are modelled on Committee Publication Ethics (COPE) Guidelines Principles...

Hemophilia is a X-linked recessive disorder of the coagulation cascade, that results in deficiency clotting factors VIII and IX, with prevalence one 5000 to 30,000 live births, type A B respectively. Factor replacement therapy remains mainstay treatment along supportive measures but often associated development alloantibodies against transfused factors, resulting suboptimal response, more complications, increased expenditure as result compromising quality life. Methodology: In this hospital...

Abstract Background Despite the availability of factor replacement therapy, including prophylaxis, to treat and prevent bleeding, haemophilic arthropathy continues be most common complication haemophilia significantly impairs quality life in people with (PwH). Regular periodic assessment joint status PwH is essential identify early arthropathic changes development or progression arthropathy. Kinematic kinetic are preferable MRI gold standard for diagnosing arthropathy, but limited developing...

Leptospirosis is a zoonotic disease that predominantly occurs in tropical and subtropical areas. It caused by the spirochete Leptospira interrogans complex may lead to syndromes can vary from subclinical infection or mild febrile severe icterohemorrhagic condition. This case report on 52-year-old farmer who had presented with upper gastrointestinal (GI) bleed. He was initially thought be of complications Chronic Liver Disease. However, he later found have icterus, renal failure, hemorrhagic...

Abstract Haemophilia is an inherited X-linked bleeding disorder characterised by a deficiency or absence of clotting factor VIII (haemophilia A) IX B), which can cause musculoskeletal bleeding. The standard treatment for haemophilia with concentrates to replace the missing deficient factor. However, there risk that immune system develops antibodies against exogenous factor, known as inhibitors. Managing patients and inhibitors who develop in unusual sites be challenging treating physician....

Primary Sjogren's syndrome (pSS) is a chronic systemic autoimmune rheumatic disorder that characterized by lymphoplasmacytic infiltration of the salivary and lacrimal glands. pSS most frequent connective tissue after rheumatoid arthritis, affecting 0.3%–3% population. The prevalence more common in women than men, with sex ratio 9:1. Occult can rarely present as immune-mediated cytopenia. In this case report, we exemplify an atypical presentation presented thrombocytopenia. Hence, should...